Article
Noninsulinoma pancreatogenous hypoglycaemia in adults--a spotlight on its genetics.
Endokrynologia Polska - 1 Jan 2015
Gilis-Januszewska Aleksandra, Piątkowski Jakub, Skalniak Anna, Piwońska-Solska Beata, Nazim Joanna, Pach Dorota, Przybylik-Mazurek Elwira, Sowa-Staszczak Anna, Starzyk Jerzy, Hubalewska-Dydejczyk Alicja
Abstract excerpt
Hyperinsulinaemic hypoglycaemia (HH) is also classically referred to as "nesidioblastosis". Heterogeneous clinical manifestation of the disease causes risk of late diagnosis or even misdiagnosis. In infants and children, it can lead to serious and permanent damage to the central nervous system, which leads to the manifesting mental retardation. HH is characterised by unregulated insulin secretion from pancreatic...
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