Article
Quantifying behaviors of children with Sanfilippo syndrome: the Sanfilippo Behavior Rating Scale.
Molecular genetics and metabolism - 1 Apr 2015
Shapiro Elsa G, Nestrasil Igor, Ahmed Alia, Wey Andrew, Rudser Kyle R, Delaney Kathleen A, Rumsey Robin K, Haslett Patrick A J, Whitley Chester B, Potegal Michael
Abstract excerpt
The Sanfilippo Behavior Rating Scale (SBRS), a 68 item questionnaire, has been developed to assess the behavioral phenotype of children with Sanfilippo syndrome and its progression over time. Fifteen scales rate orality, movement/activity, attention/self-control, emotional function including anger and fear, and social interaction. Items within scales intercorrelate; measures of internal consistency are adequate....
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