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Article

Phenotypic variation and long-term outcome in children with congenital hepatic fibrosis.

Journal of pediatric gastroenterology and nutrition - 1 Aug 2013

Rawat Dinesh, Kelly Deirdre A, Milford David V, Sharif Khalid, Lloyd Carla, McKiernan Patrick J

Abstract excerpt

BACKGROUND AND OBJECTIVE: Congenital hepatic fibrosis (CHF) and Caroli syndrome are frequently associated with renal cystic diseases. They have a variable clinical course, and the natural history is not well defined despite molecular advances. Our study describes the clinical manifestations and l...

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PMID: 23518487
DOI: 10.1097/MPG.0b013e318291e72b

Provenance

PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 4 Sept 2026. Prepared record publication-23518487-2026-09-04.2. Manifest publication-graph-cohort-2026-09-04.2.

Source receipt: PubMed via Helena Literature Corpus, retrieved 4 Sept 2026.

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