Article
[Orbitotemporal facial involvement in type 1 neurofibromatosis (NF1)].
Neuro-Chirurgie - 1 Jan 2000
Rilliet B, Pittet B, Montandon D, Narata A-P, de Ribaupierre S, Schils F, Boscherini D, Di Rocco C, Ducrey N
Abstract excerpt
Plexiform neurofibromas of the orbit, sometimes extending to the temporal region and the face, are considered to be a rare but devastating and disfiguring complication of neurofibromatosis type 1. The first symptoms appear in infancy and the involvement of the orbit and the face is present in nearly all children after the age of 5. The disease is unilateral in most cases but can exceptionally involve both sides...
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