[Postoperative complications in a man with San Filippo syndrome anesthetized for multiple tooth extraction].

Abstract excerpt

San Filippo syndrome is a hereditary lysosomal disorder resulting in the accumulation of mucopolysaccharides (mucopolysaccharidosis type II). A deficit in the enzyme required to break down heparan sulfate leads to its deposition in the connective tissue of many organs, particularly the brain, liver, heart, and spleen. The first symptoms-including mental deterioration, dimorphism, and behavioral changes such as...

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