Article
[Malignancy risk and Wiedemann-Beckwith syndrome: what follow-up to provide?].
Archives de pediatrie : organe officiel de la Societe francaise de pediatrie - 1 Sept 2008
Santiago J, Muszlak M, Samson C, Goulois E, Glorion A, Atale A, Ranaivoarivony V, Hebert J-C, Bouvier R, Cordier M-P
Abstract excerpt
Wiedemann-Beckwith syndrome (WBS) is a syndrome of excessive growing with a high predisposition to developing embryologic tumours within the first years of life. This risk is evaluated between 7.5 and 10%; it varies with the mechanisms of mutations involved. These take place in two distinct domai...
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