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Article

Neuropathological findings in a Staffordshire bull terrier with l-2-hydroxyglutaric aciduria.

Journal of comparative pathology - 1 Jan 2000

Scurrell E, Davies E, Baines E, Cherubini G B, Platt S, Blakemore W, Williams A, Schöniger S

Abstract excerpt

l-2-Hydroxyglutaric aciduria (l-2-HGA) is a hereditary neurometabolic disorder reported in human beings and dogs. An 11-month-old Staffordshire bull terrier was suspected to have the disease, on the basis of clinical signs and magnetic resonance imaging findings. l-2-HGA was confirmed by urinary organic analysis and DNA testing and the dog was humanely destroyed. Post-mortem findings consisted only of...

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PMID: 18295785
DOI: 10.1016/j.jcpa.2007.11.005

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-08.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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