Article
Rendu-Osler-Weber disease: update of medical and dental considerations.
Oral surgery, oral medicine, oral pathology, oral radiology, and endodontics - 1 Feb 2008
te Veldhuis E C, te Veldhuis A H, van Dijk F S, Kwee M L, van Hagen J M, Baart J A, van der Waal I
Abstract excerpt
Rendu-Osler-Weber disease, also known as hereditary hemorrhagic telangiectasia (HHT), is an autosomal dominant inherited disorder characterized by an aberrant vascular development. The reported prevalence is approximately 1 per 5,000-10,000. The clinical manifestations consist of recurrent spontaneous nosebleeds, telangiectasias characteristically at the lips, oral cavity, fingers, and nose, and visceral...
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