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Article

Early pulmonary manifestation of cystic fibrosis in children with the DeltaF508/R117H-7T genotype.

Pediatrics - 1 Sept 2006

O'Sullivan Brian P, Zwerdling Robert G, Dorkin Henry L, Comeau Anne Marie, Parad Richard

Abstract excerpt

We report 3 cystic fibrosis newborn screen-positive infants with the DeltaF508/R117H-7T genotype who had Pseudomonas aeruginosa detected in oropharyngeal cultures early in life and a fourth who had pulmonary symptoms and Gram-negative growth on multiple oropharyngeal cultures. All 4 patients were...

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Source

Identifiers

PMID: 16951024
DOI: 10.1542/peds.2006-0399

Provenance

PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 2 Sept 2026. Prepared record publication-16951024-2026-09-02.2. Manifest publication-graph-cohort-2026-09-02.2.

Source receipt: PubMed via Helena Literature Corpus, retrieved 2 Sept 2026.

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Early pulmonary manifestation of cystic fibrosis in children with the DeltaF508/R117H-7T genotype.PMID 16951024Read ↗

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