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Article

Considerations in the difficult-to-manage urea cycle disorder patient.

Critical care clinics - 1 Oct 2005

Lee Brendan, Singh Rani H, Rhead William J, Sniderman King Lisa, Smith Wendy, Summar Marshall L

Abstract excerpt

Today, patients with urea cycle disorder (UCD) may survive well beyond infancy. The goal of keeping them in consistent nitrogen balance can be undermined by changing metabolic needs throughout various stages of life, resulting in hyperammonemia in the short term, and poor growth and development in the long term. The specific UCD genotype can affect the risk of metabolic destabilization and management...

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Share to Amino Acid Metabolism, Inborn Errors
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Methodology Data sources Editorial policy Privacy About Contact Helena Bioinformatics

Share to Ornithine Carbamoyltransferase Deficiency Disease

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Identifiers

PMID: 16227112
DOI: 10.1016/j.ccc.2005.05.001

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-07.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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