Article
Diamond-Blackfan anemia.
Current opinion in pediatrics - 1 Feb 2001
Da Costa L, Willig T N, Fixler J, Mohandas N, Tchernia G
Abstract excerpt
Diamond-Blackfan Anemia (DBA) is a rare, congenital hypoplastic anemia often diagnosed early in infancy. A moderate to severe aregenerative anemia is found in association with erythroblastopenia in an otherwise normocellular bone marrow. In 40% of these infants with DBA, diverse developmental abnormalities are also noted. A majority of patients with DBA respond to steroid therapy. Recent molecular studies have...
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