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Article

Progressive myoclonus epilepsy of Unverricht-Lundborg type.

Epilepsia - 1 Jan 1999

Lehesjoki A E, Koskiniemi M

Abstract excerpt

Progressive myoclonus epilepsy of Unverricht-Lundborg type (EPM1) is characterized by onset at age 6-15 years, stimulus-sensitive myoclonus, tonic-clonic seizures, and typical EEG findings, with marked sensitivity to photic stimulation. Previously the course of the disease was progressive throughout the life, and no biochemical or pathologic marker existed for the diagnosis of EPM1. With modern anticonvulsive...

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Identifiers

PMID: 10446747
DOI: 10.1111/j.1528-1157.1999.tb00895.x

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