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Article

Enteroviral meningoencephalitis as a complication of X-linked hyper IgM syndrome.

The Journal of pediatrics - 1 May 1999

Cunningham C K, Bonville C A, Ochs H D, Seyama K, John P A, Rotbart H A, Weiner L B

Abstract excerpt

We describe 5 children from 2 families with mutations in the CD40 ligand (CD40L) gene leading to absent expression of CD40L on activated CD4 cells. All subjects presented with interstitial pneumonia with low serum IgG and normal serum IgM. One child had normal and one child had elevated serum IgA. Four had confirmed Pneumocystis carinii pneumonia. In spite of intravenous immunoglobulin treatment yielding...

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Methodology Data sources Editorial policy Privacy Delete account & data About Contact Helena Bioinformatics

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Source

Identifiers

PMID: 10228294
DOI: 10.1016/s0022-3476(99)70245-3

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-08.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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